{"id":4592,"date":"2022-10-30T18:22:21","date_gmt":"2022-10-30T17:22:21","guid":{"rendered":"https:\/\/sfrms-app.fr\/?p=4592"},"modified":"2022-10-30T19:14:38","modified_gmt":"2022-10-30T18:14:38","slug":"specificites-de-lenfant-4","status":"publish","type":"post","link":"https:\/\/sfrms-app.fr\/index.php\/2022\/10\/30\/specificites-de-lenfant-4\/","title":{"rendered":"Sp\u00e9cificit\u00e9s de l&rsquo;enfant"},"content":{"rendered":"<h2 class=\"wp-block-heading\">Narcolepsie de l&rsquo;enfant<\/h2>\n\n\n\n<p><strong>S&eacute;miologie somnologique<\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\"><li><a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/term-test-2\/\" title=\"Glossary: Acc&egrave;s de sommeil\" class=\"glossaryLink\">Acc&egrave;s de sommeil<\/a> d&rsquo;apparition brutal, possiblement long et peu rafraichissant.<\/li><li>Augmentation du temps de <a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/sommeil\/\" title=\"Glossary: Sommeil\"  class=\"glossaryLink\">sommeil<\/a> et <a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/inertie-du-sommeil\/\" title=\"Glossary: Inertie du sommeil\" class=\"glossaryLink\">inertie du sommeil<\/a> possible.<\/li><li>R&eacute;apparition ou persistance des siestes au de la de 6 ans et <a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/endormissement\/\" title=\"Glossary: Endormissement\" class=\"glossaryLink\">endormissement<\/a> en classe.<\/li><li>Sympt&ocirc;mes d&rsquo;inattention et\/ou <a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/hyperactivite\/\" title=\"Glossary: Hyperactivit&eacute;\" class=\"glossaryLink\">hyperactivit&eacute;<\/a> (expression de la <a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/somnolence\/\" title=\"Glossary: Somnolence\"  class=\"glossaryLink\">somnolence<\/a> diurne excessive)<\/li><\/ul>\n\n\n\n<p><strong>S&eacute;miologie associ&eacute;e<\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\"><li><a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/cataplexie\/\" title=\"Glossary: Cataplexie\"  class=\"glossaryLink\">Cataplexie<\/a> d&eacute;clench&eacute;e parfois sans facteur &eacute;motionnel, souvent fluctuante.<\/li><li><strong>Cataplexie avec chute de la t&ecirc;te et\/ou faci&egrave;s cataplectique <\/strong>(particuli&egrave;rement lors des 6 premiers mois de la maladie) :<ul><li>Signes n&eacute;gatifs : hypotonie de la face, des paupi&egrave;res et de la bouche avec protrusion de la langue, chute de la t&ecirc;te,<\/li><\/ul><ul><li>Signes positifs : lev&eacute; de sourcils, grimaces faciales, mouvements p&eacute;rioraux et de la langue, dyskin&eacute;sie et mouvements dystoniques de la face, balancement de la t&ecirc;te et du tronc.<\/li><\/ul><ul><li>https:\/\/www.narcolepsylink.com\/pediatric\/recognize\/narcolepsy-symptoms\/<\/li><\/ul><\/li><li>Prise de poids marqu&eacute; avec possible ob&eacute;sit&eacute; dans plus de 50 % des cas (souvent d&egrave;s le d&eacute;but de la maladie).<\/li><li>Mauvaise qualit&eacute; de sommeil \/ Insomnie de maintien du sommeil.<\/li><li>Parasomnies en sommeil lent ou paradoxal<\/li><\/ul>\n\n\n\n<p><strong><a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/diagnostic\/\" title=\"Glossary: Diagnostic\"  class=\"glossaryLink\">Diagnostic<\/a><\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\"><li>Recherche d&rsquo;une <a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/hypersomnie\/\" title=\"Glossary: Hypersomnie\" class=\"glossaryLink\">hypersomnie<\/a> centrale secondaire : <strong>IRM c&eacute;r&eacute;brale<\/strong>. <\/li><li><strong>TILE: Latence &lt; 8 min et\/ou 2 SOREM<\/strong>, avec si n&eacute;cessaire r&eacute;p&eacute;tition de l&rsquo;&eacute;valuation dans un d&eacute;lai de 6 &agrave; 24 mois, car parfois absence des crit&egrave;res au TILE en d&eacute;but de maladie.<\/li><\/ul>\n\n\n\n<p><strong>Comorbidit&eacute;s<\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\"><li>Troubles de l&rsquo;<a href=\"https:\/\/sfrms-app.fr\/index.php\/glossary\/humeur\/\" title=\"Glossary: Humeur\"  class=\"glossaryLink\">humeur<\/a>.<\/li><li>Troubles des apprentissages scolaires.<\/li><\/ul>\n\n\n\n<p><strong>Prise en charge<\/strong><\/p>\n\n\n\n<p>&Eacute;valuation multidisciplinaire en centre de r&eacute;f&eacute;rence, narcolepsie et hypersomnie rare sp&eacute;cialis&eacute; de l&rsquo;enfant.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Narcolepsie de l&rsquo;enfant S&eacute;miologie somnologique Acc&egrave;s de sommeil d&rsquo;apparition brutal, possiblement long et peu rafraichissant. Augmentation du temps de sommeil et inertie du sommeil possible. R&eacute;apparition ou persistance des siestes au de la de 6 ans et endormissement en classe. [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":4061,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[24],"tags":[],"class_list":["post-4592","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-troubles-hypersomnolence-dorigine-centrale"],"featured_image_src":"https:\/\/sfrms-app.fr\/wp-content\/uploads\/2021\/11\/UTwTq5an_normal.png","blog_images":{"medium":"https:\/\/sfrms-app.fr\/wp-content\/uploads\/2021\/11\/UTwTq5an_normal.png","large":"https:\/\/sfrms-app.fr\/wp-content\/uploads\/2021\/11\/UTwTq5an_normal.png"},"_links":{"self":[{"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/posts\/4592","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/comments?post=4592"}],"version-history":[{"count":2,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/posts\/4592\/revisions"}],"predecessor-version":[{"id":4597,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/posts\/4592\/revisions\/4597"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/media\/4061"}],"wp:attachment":[{"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/media?parent=4592"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/categories?post=4592"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/sfrms-app.fr\/index.php\/wp-json\/wp\/v2\/tags?post=4592"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}